Nutritional Information

Energy Distribution

Fat46%
Carbohydrate44%
Protein10%

Sources

Protein: Mixture of pure L-amino acids
Fats: Corn oil, DHA and ARA powder
Carbohydrates: Maltodextrin and starch

At a Glance

Energy: 493 Kcal per 100 g
Per serving: 64 Kcal
Serving Size: 13
Gluten free
Lactose free
Osmolarity: 315 mOsm/L
Osmolality: 330 mOsm/kg
Scoop size: 4.3 grams

Nutritional Table

Nutrient	Unit	Per 100 mL	Per 100 g
Energy	kJ	268.19	2063
Energy	kcal	64.09	493
Fat	g	3.25	25
Saturated fatty acids	g	1.2025	9.25
Monounsaturated fatty acids	g	1.56	12
Polyunsaturated fatty acids	g	0.4875	3.75
linoleic acid	g	0.455	3.5
α-linolenic acid	g	0.065	0.5
arachidonic acid	mg	6.5	50
docosahexaenoic acid	mg	6.5	50
Carbohydrate	g	7.02	54
Added sugars	g	0	0
Protein	g	1.69	13
L-Alanine	g	0.0988	0.76
L-Arginine	g	0.1092	0.84
L-aspartic acid	g	0.1274	0.98
L-Cystine	g	0.0546	0.42
L-Glutamic acid	g	0.195	1.5
L-Glutamine	g	0.0494	0.38
Glycine	g	0.0936	0.72
L-Histidine	g	0.0585	0.45
L-Isoleucine	g	0	0
L-Leucine	g	0	0
L-Lysine	g	0.169	1.3
L-Methionine	g	0.039	0.3
L-Proline	g	0.1625	1.25
L-Serine	g	0.1261	0.97
L-Threonine	g	0.117	0.9
L-Tryptophan	g	0.039	0.3
L-Tyrosine	g	0.169	1.3
L-Valine	g	0	0
Sodium	mg	16.25	125
Potassium	mg	58.5	450
Chloride	mg	39	300
Calcium	mg	58.5	450
Phosphorous	mg	31.2	240
Magnesium	mg	8.45	65
Iron	mg	0.845	6.5
Zinc	mg	0.689	5.3
Copper	mg	0.0455	.35
Iodine	mcg	11.05	85
Chromium	mcg	1.365	10.5
Fluoride	mcg	0	0
Manganese	mg	0.052	0.4
Molybdenum	mcg	3.9	30
Selenium	mcg	2.6	20
Vitamin A	mcg	97.5	750
Vitamin D	mcg	1.3	10
Vitamin E	mg	1.3	10
Vitamin K	mcg	5.2	40
Vitamin C	mg	9.75	75
Vitamin B1/Thiamine	mg	0.0585	0.45
Vitamin B2/Riboflavin	mg	0.1235	0.95
Niacin	mg	0.715	5.5
Vitamin B6	mg	0.0676	0.52
Folate (DFE)	mcg	13	100
Pantothenic acid	mg	0.4875	3.75
Vitamin B12	mcg	0.195	1.5
L-Carnitine	mg	1.95	15
Choline	mg	3.9	30
Inositol	mg	11.05	85
Taurine	mg	3.9	30
Biotin	mcg	5.2	40

Serving Size: 13.

Ingredients

Maltodextrine, Vegetable oils (Corn oil, sunflower oil), Starch, L-Lysine-L-Glutamate, L-Lysine-LAspartate, L-Arginine-L-Aspartate, L-Proline, tri-Calcium phosphate, L-Serine, L-Threonine, Emulsifier E472c, tri Potassium citrate, L-Alanine, Glycine, L-Tyrosine, L-Phenylalanine, L-Glutamic acid, L-Histidine, L-Cystine, L-Glutamine, L-Tryptophan, L-Methionine, Sodium chloride, Potassium chloride, Oil from Mortierella alpina, Magnesium carbonate, Choline bitartrate, DHA and EPA-rich oil from the microalgae Schizochytrium sp., di Calcium phosphate, Vitamins (A, D, E, K, C, B1, B2, Niacin, B6, Folic acid, Pantothenic acid, B12, Biotin), Inositol, L-Carnitine-L-Tartrate, Taurine, Iron-II-sulfate, Zinc sulfate, Emulsifier lecithine, Antioxidants Tocopherol-rich extract and Ascorbyl palmitate, Manganese sulfate, Copper sulfate, Sodium fluoride, Potassium iodide, Sodium molybdate, Chromium-III-chloride, Sodium

Allergens: No allergen present

Indications and Warnings

Indication

For the dietary management of Disorders in Branched Chain Amino Acid Metabolism (Maple syrup urine disease) in infancy. It consists of an isoleucine-, leucine-and valine-free amino acid mixture, carbohydrates and a special fat blend containing long chain polyunsaturated fatty acids (LCP), and is supplemented with vitamins, minerals, and trace elements. Carnitine.

Warnings and precautions

Not suitable for use as a sole source of nutrition
Must be used under medical supervision.
Not to be used by individuals without disorders in branched chain amino acid metabolism.
Not suitable for parenteral use
Not suitable for patients with galactosaemia
Do not boil mixture or use terminal sterilisation.
Never use a microwave oven to warm formula.
Serious burns can result.

Instructions for Use

Preparation

PREPARATION (standard dilution)
Pour required volume of hot previously boiled water (cooled down to 50 °C) into a feeding bottle.
Add measured amount of MSUD A formula and, if applicable, normal infant formula, close the bottle and shake well until the powder dissolves.
Before feeding, ensure that the formula is at the correct temperature by placing a few drops on the inside of your wrist.
Prepare feed always fresh and discard unfinished feeds.
Please watch dental care, especially before bedtime.

Directions for use

Oral / Tube Feeding
The daily amount of MSUD A formula required should be divided into 3 to 5 single portions and should be taken with mixed with breast milk or normal infant formula in calculated amounts.
Diets with MSUD A formula must contain adequate amount of energy, essential fatty acids, isoleucine and valine to meet daily requirements.
The recommended dosage and timing of intake is dependent on the age, bodyweight, and medical condition of the patient, and should be determined by a dietitian or clinician only.
Mixing ratio - Depending on specific needs of everyone, preparation will vary as prescribed by healthcare personnel, Dietitians or medical practitioner.

Storage and Product Details

Store in a cool, dry place (5-25°C).
Always replace the lid after use.
Once opened, use within two weeks.

Shelf life: 18 months
Catalogue number: ME110
Barcode (GTIN): 06287043710408

MetaEnergy MSUD A